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9
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Wszystko
o hemofilii
Poradnik
dla
rodziny
9
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Wszystko
o hemofilii
Poradnik
dla
rodziny
9–2
9
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Tabela 1
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"&<//&,47(X#L!(.&<(+*'0+9JB(L!(-'.)I2&(/01'1&!-&!(&(-&/)(=#(#*(0'+5(
-&!(0#+2#+-'B('-&(-&!(;<*+&!(1&'*#"#B(,#(:!(.2#1#*#1'?#7(
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.I(19-&/&!"(*0#;-9,4(50'+H1B(-27(/#-)5+:&(.2#0)#19,47(M&!"-&!:(
:!*-'/(5(-&!/)H09,4(#.H;(,4#09,4(-'(5"&'0/#1'-I(4!"#$%&<B(
+1?'.+,+'(5()9,4B(5(/)H09,4(2#+&#"(,+9--&/'(EFFF(%5;(F6(19-#.&(
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Nadal jest
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dlaczego u niektórych
dzieci chorych
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Wszystko
o hemofilii
9–3
Poradnik
dla
rodziny
9
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Tabela 2
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Wszystko
o hemofilii
Poradnik
dla
rodziny
9–4
9
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]9"'='-9(:!.)(2#"&'0('/)91-#3,&(,+9--&/'(/0+!2-&<,&'(1!(/01&7(
C'/&!(;'*'-&!(-&!(:!.)(#=H%-&!(*#.)<2-!(1("'?9,4(%';#0')#0&',4(
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.2!,:'%&.)9,+-!=#(#30#*/'B(/)H09(2#)1&!0*+&(*&'=-#+<7(_#+2#+-'-&!(
?'=#*-!:(&(5"&'0/#1'-!:(4!"#$%&&(D(19"'='(2#-'*)#(0HL-&,#1'-&'(
+(,4#0#;I(`#-(]&%%!;0'-*'B(,+9%&(#+-',+!-&'('/)91-#3,&(,+9--&/'(
`#-(]&%%!;0'-*'(1!(/01&7(G'*'-&!()#(:!.)(:!.+,+!()05*-&!:(*#.)<2-!(
-&L(;'*'-&'('/)91-#3,&(,+9--&/'(EFFF(&(F67(
P#:'1&'(.&<(1&!%!(*#-&!.&!a(#(#.#;',4B(5(/)H09,4(-&!(+*&'=-#+#1'-#(
4!"#$%&&(*#("#"!-)5(#.&I=-&<,&'(20+!+(-&!(*#0#.?#3,&7(>4#J("#L-'()#(
)0'/)#1'J(:'/#(*#;09(+-'/B(L!(,4#0#;'(20+!;&!='(?'=#*-&!B()#(+(*05=&!:(
.)0#-9(,+'.!"(4!"#$%&'("#L!(2#+#.)'J(-&!19/09)'('L(*#(192'*/5(
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%!/'0+(0#*+&--9(2#*!:0+!1',&!(5(*+&!,/'(./'+<(/01#)#,+-IB(-'%!L9(
5*'J(.&<(*#(.+2&)'%'B(/)H09(.2!,:'%&+5:!(.&<(1(0#+2#+-'1'-&5(&(%!,+!-&5(
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.2!,:'%&3,&(20+!20#1'*+I(&-*91&*5'%-9(191&'*B(#,!-&I(4&.)#0&<(
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:'/(-':.+9;.+!(0#+2#+-'-&!(,4#0#;97(M&!(,+!/':B('L(2#:'1&(.&<(2#1'L-!(
/01'1&!-&!(1(-'=?!:(.9)5',:&7
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ma 12 lat i wymaga
leczenia kilka razy
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z innymi rodzinami
i dostrzeganie, jak
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,4#0#;I7(O-&()!L(2#1&--&("&!J(2#.)'1&#-I(*&'=-#+<(-'(192'*!/B(
=*9;9(+*'0+9?#(&"(.&<(2#1'L-!(/01'1&!-&!(%5;(50'+("#=I,9(
+'=0#+&J(L9,&57
Wszystko
o hemofilii
9–5
Poradnik
dla
rodziny
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
n &B!+'2&'./%'28:&#-;82&42;72%'!&$4!&/6;1&*#$7!8@,&12)#34''?&
P0#;%!"!"(1(4!"#$%&&(:!.)(;0'/(%5;(-&./&(2#+&#"(,+9--&/H1(
/0+!2-&<,&'c(,+9--&/'(EFFF(1(20+92'*/5(4!"#$%&&()925(D(%5;(,+9--&/'(
F6(1(4!"#$%&&()925(G7(>!%!"(%!,+!-&'(*+&!,&(,4#09,4(-'(4!"#$%&<(:!.)(
+'2#;&!='-&!(/01'1&!-&#"7(>+'.!"(:!*-'/B("&"#(-':1&</.+9,4(
19.&?/H1B(/01'1&!-&'("#=I(.&<(+*'0+'J7(](20+92'*/5(19.)I2&!-&'(
/01'1&!-&'(-'%!L9(.+9;/#(+'.&<=-IJ(2#0'*9(%!/'0+'(&(2#*:IJ(*+&'?'-&'(
+"&!0+':I,!(*#(+1&</.+!-&'(2#+&#"5(;0'/5:I,!=#(,+9--&/'(
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Wszystko
o hemofilii
Poradnik
dla
rodziny
9–6
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
M&!1&!%/'(%&,+;'(,4#09,4(-'(5"&'0/#1'-I(2#.)'J(4!"#$%&&B(
+1?'.+,+'()9,4B(5(/)H09,4('/)91-#3J(,+9--&/'(EFFF(%5;(F6(
-&!(20+!/0',+'(YSB(19"'='(0!=5%'0-!=#(2#*'1'-&'(/#-,!-)0')H1(
,+9--&/'7(U(1&</.+#3,&(,4#09,4(-'(5"&'0/#1'-I(4!"#$%&<(-&!1&!%/&!(
/01'1&!-&'(-&!(19"'=':I(2#*'1'-&'(,+9--&/H1(/0+!2-&<,&'7(
](1&!%5(192'*/',4("#L-'(.)#.#1'J(&--!("!)#*9(%!,+!-&'B(';9(
+"-&!:.+9J(%5;(19!%&"&-#1'J(/#-&!,+-#3J(5L91'-&'(/#-,!-)0')H1(
,+9--&/'7(
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/"9,-%)*H$#%:-<*:-%("*(*4#I%4%<#=*&$'E%;')*?.22A%G*("7+$-%#',*0*.%
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$#%)*!094/7%+,*(">A%
Wszystko
o hemofilii
9–7
Poradnik
dla
rodziny
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
P%Q*.(!'%E'("%"'H%&*("7+$#%&'()*+,'(-$#%4%+*("#!2%&*3("$'E%
1"#:.'"/2%R2$2,2$56%/"9,>%("*(3E'%(27%E#/*%.'/%#$"-&23,'"-!0$-%4%.'!0'$23%
)2)*4*.$'=*%)*!0'$2#%$*!$'=*A%T2'%E'("%*$#%E'&$#/%(/3"'!0$#%
4%(/#0#!;%/,4*"*!0$-!;A
G'()*+,'(-$#%+*&#$#%&*H-.$2'6%&*$*(*4*%.3:%+*&(/9,$2'%)*H'%*/*<*%
",0-/,*"$2'%0427/(0-I%+*02*)%!0-$$2/#%CDDD%4'%/,42A%G027/2%"')3%
)*H'%(/3"'!0$2'%0#+*:2'=#I%/,4#42'$2*)%*,#0%.'!0-I%E'%3%427/(0*8!2%
!;*,-!;%$#%<#=*&$>%;')*?.27%@A%Q,0'&%0#("*(*4#$2')%&'()*+,'(-$-%
.'/#,0%0%*8,*&/#%.'!0'$2#%;')*?.22%0#.'!2%!;*,')3%4-/*$#$2'%"'("3%
*&+*42'&02%$#%.'/A%Q*.'=#%*$%$#%+*&#$23%Z+,9:$'E[%&#4/2%.'/3%
2%0)2',0'$23%#/"-4$*8!2%!0-$$2/#%CDDD%+*%3+<-42'%LMN\M%)2$3"%
*&%0#/*F!0'$2#%/,*+.94/2A%Q*04#.#%"*%*!'$2I6%E#/%&#$#%*(*:#%,'#=3E'%
$#%.'/%N%!0-%:7&02'%*$%3%$2'E%(/3"'!0$-A
T2'("'"-6%&02#<#$2'%&'()*+,'(-$-%042>0#$'%0'%0427/(0#$2')%+*02*)3%
!0-$$2/#%CDDD%E'("%/,9"/*",4#<'A%R#/(-)#.$#%*&+*42'&]%$#("7+3E'%
0#04-!0#E%4%!2>=3%=*&02$-%*&%+*&#$2#%.'/36%!;*I%!078!2*4*%E'E%
&02#<#$2'%3",0-)3E'%(27%$#4'"%+*%X^%=*&02$#!;A%G'()*+,'(-$7%)*H$#%
+*$*4$2'%+*&#I%+*%!*%$#E)$2'E%X^N^O%=*&02$#!;6%#.'%E'E%("*(*4#$2'%
E'("%)*H.24'%"-./*%+,0'0%/2./#%&$2%0%,07&3A%Q*%"-)%!0#(2'%(/3"'!0$*8I%
+,'+#,#"3%0#$2/#6%=&-H%4-!0',+3E>%(27%0#+#(-%!0-$$2/#%CDDD%
0)#=#0-$*4#$'=*%+,0'0%*,=#$20)A%B'8.2%&*%/*$",*.2%/,4#42'F%
/*$2'!0$'%E'("%&#.(0'%.'!0'$2'6%+,#4&*+*&*:$2'%+*",0':$'%:7&>%
/*$!'$",#"-%!0-$$2/#A%Q*%/2./3%&$2#!;%+,0',4-%4%.'!0'$23%
&'()*+,'(-$>%)*H$#%+*&#4#I%E>%0$*436%+*$2'4#H%*,=#$20)%0&*<#<%
E3H%*&$*42I%0#+#(-%!0-$$2/#%CDDDA%
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Wszystko
o hemofilii
Poradnik
dla
rodziny
9–8
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
G'()*+,'(-$#%)#%"'H%&02#<#$2'%#$"-&23,'"-!0$'J%+*4*&3E'%
0)$2'E(0'$2'%2.*8!2%4-&#.#$'=*%)*!03%2%0#",0-)#$2'%4*&-%
4%*,=#$20)2'A%_%)#<-!;%&02'!26%/"9,'%(+*H-4#E>%&3H'%2.*8!2%+<-$94%
14*&-6%(*/26%).'/*%2"+A5%"'$%(/3"'/%3:*!0$-%+,'+#,#"3%)*H'%+,*4#&02I%
&*%;2+*$#",')22J%("#$36%4%/"9,-)%0#4#,"*8I%(*&3%.3:%(*.2%4%
*,=#$20)2'%E'("%$2(/#A%P%,0#&/2!;%+,0-+#&/#!;%&'()*+,'(-$#%)*H'%
4-4*<#I%&,=#4/26%&.#"'=*%E'8.2%+*&#E'%(27%"'$%.'/6%04<#(0!0#%:#,&0*%
)#<-)%&02'!2*)6%4#H$'%E'("%E'&$*!0'($2'%3$2/#$2'%+*&#4#$2#%2)%
&3H'E%2.*8!2%+<-$94A%_%)#<-!;%&02'!2%$#.'H-%"'H%(+,#4&0#I%+*02*)%
(*&3%4'%/,42A%
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;')*?.22`%
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/*$2'!0$*8I%("*(*4#$2#%/*$!'$",#"94%!0-$$2/#%/,0'+$27!2#%
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;')*?.226%#:-%&*42'&02'I%(276%!0-%.'!0'$2'%&'()*+,'(-$>%(+,#4&02%(27%
4%+,0-+#&/3%a4*E'=*%&02'!/#6%E#/#%:-<#:-%&.#%$2'=*%$#E.'+(0#%+*("#I%
&'()*+,'(-$-%2%E#/%E>%+*&#4#IA%
Wszystko
o hemofilii
9–9
Poradnik
dla
rodziny
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
D'15%#$"-B6,-$*<5"-!0$'%.("*(*/#$'%0#,?/$*%/%<'!0'$52%$5'&*6*,2%
!0-$$51#%7888E%@#1%8F9
K'/2%#$"-?:,-$*.2"-!0$'6%E#/%$+A%/4#(%",#$'/(#)*4-%1+,'+#,#"%
bc#!-.5%"#/H'%+*)#=#E>%4%.'!0'$23%;')*?.226%0#,94$*%"-+3%@6%E#/%2%dA%
D$$-)%"#/2)%.'/2')%E'("%/4#(%ef#)2$*/#+,*$*4-%1b@g@56%#.'%$2'%E'("%
*$%E3H%&*("7+$-%4%Q*.(!'A
G02#<#$2'%"-!;%+,'+#,#"94%+*.'=#%$#%40)#!$2#$23%
+*4("#E>!-!;%(/,0'+946%!*%0#+*:2'=#%2!;%
*&,-4#$23%2%+*$*4$')3%,*0+*!07!23%(27%
/,4#42'$2#A%h,*&/2%#$"-?:,-$*.2"-!0$'%(>%
(0!0'=9.$2'%+,0-&#"$'%4%.'!0'$23%/,4#42'F%4%E#)2'%
3("$'E%10%&02>('<6%07:94%!0-%E70-/#5%*,#0%/,4*"*/94%
0%$*(#A%T2'%(>%*$'%0#.'!#$'%+,0-%/,4#42'$2#!;%
0%&,9=%)*!0*4-!;6%+*$2'4#H%)*=>%+,*4#&02I%
&*%+*4("#$2#%(/,0'+36%/"9,-%4%+*&*:$-%(+*(9:6%
E#/%/#)2'$2'%$',/*4'6%:.*/3E'%+,0'+<-4%)*!03A%%
+ !"#$%"&'()#*+,-./#+01234(-/+##0(#5.4(5#
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+*&%*+2'/>%?0E*"',#+'3"-6%)#E>!'=*%&*842#&!0'$2'%4%+,#!-%0%*(*:#)2%
0%">%!;*,*:>A%j20E*"',#+'3"#%0%*8,*&/#%.'!0'$2#%;')*?.22%+*)*H'%a*:2'%
2%&02'!/3%$#3!0-I%(27%,*0+*0$#4#I%2%.'!0-I%/,4#42'$2#%&*%("#494%
2%)278$2%*,#0%&*,#&026%E#/2'%I42!0'$2#%2%V*,)-%#/"-4$*8!2%?0-!0$'E%
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Q*)+,'((2*$6%R.'W#"2*$5A%
Wszystko
o hemofilii
Poradnik
dla
rodziny
9–10
9
l
l
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
&+*!0-$'1=%T#.'H-%0#+'4$2I%*&+*!0-$'/%/*F!0-$2'6%4%/"9,'E%
$#(">+2<*%/,4#42'$2'6%=&-H%$#(2.#%(27%*$*6%E'8.2%/*F!0-$#%E'("%
$*,)#.$2'%*:!2>H#$#%2%3H-4#$#A%%
D?&=% /<#&-%0%.*&3%+*4*&3E>%047H'$2'%1*:/3,!0'$2'5%$#!0-F%
/,42*$*8$-!;6%+,0'0%!*%*=,#$2!0#E>%&*+<-4%/,42%&*%*:(0#,36%=&02'%
4-("7+3E'%/,4#42'$2'A%
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(',!#6%*:$2H#%(27%!28$2'$2'%2%0)$2'E(0#%&*+<-4%/,42%&*%)2'E(!#%
/,4#42'$2#A
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O8QR=#%2!(-%%,*0&05#3%TH%>*("I+*/#$5'%/%+,0-+#&12%1,/#/5'LE%%
JU%@#15%(+*(?6%<'!0-%(5I%1,/#/5'$5#%/'/$I",0$'MN=
P(0-("/2'%+*4-H(0'%8,*&/2%(>%2("*"$'%4%.'!0'$23%/,4#42'F%3%/#H&'=*%
&02'!/#%!;*,'=*%$#%;')*?.27A%U>%*$'%E'&$#/%4#H$2'E(0'%4%+,0-+#&/3%
&02'!2%0%<#=*&$>%+*("#!2>%!;*,*:-6%/"9,'%)*=<-%$2=&-%$2'%)2'I%
+*&#4#$'=*%/*$!'$",#"3%!0-$$2/#A
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)'"*&%.'!0'$2#%)*H'%+*04*.2I%3$2/$>I%/*$2'!0$*8!2%+*&#4#$2#%2)%
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Wszystko
o hemofilii
9–11
Poradnik
dla
rodziny
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
n 5
& !+'2&-#,'+6!%'!&)#"7&,8./7-'0&(&916#-9:,&91#*891&
%!&6!"#$%7&'&()'!*+#,!%7&-#./!0&12)#34'';
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+*4#H$'%/,4#42'$2#%+*E#42#E>%(27%,0#&/*A%k#04-!0#E%(>%*$'%
4-$2/2')%+*4#H$'=*%3,#03%:>&]%0#:2'=3%!;2,3,=2!0$'=*A%G.#"'=*%
4<#8$2'%427/(0*8I%&02'!2%!;*,-!;%$#%<#=*&$>%2%3)2#,/*4#$>%+*("#I%
;')*?.22%+,*4#&02%("*(3$/*4*%$*,)#.$'%H-!2'6%3!0'("$2!0>!%4'%
4(0'./2!;%V*,)#!;%#/"-4$*8!2A%Q,0'0%42'.'%.#"6%#%$#4'"%!0#(')%+,0'0%
!#<'%H-!2'6%)*H'%$2'%$#(">+2I%/*$2'!0$*8I%+*&#4#$2#%2)%/*$!'$",#"94%
!0-$$2/#A%R2)*%"*%E'&$#/%)*=>%)2'I%$2'*!0'/24#$'6%+*4#H$'%
/,4#42'$2#6%/"9,'%4-)#=#E>%0#("*(*4#$2#%&'()*+,'(-$-6%.'/94%
#$"-?:,-$*.2"-!0$-!;%.3:%/*$!'$",#"3%!0-$$2/#A%g0#(')%)*=>%3%$2!;%
"#/H'%4-(">+2I%+*42/<#$2#6%"#/2'%E#/%$+A%3(0/*&0'$2#%("#494%!0-%
)278$26%/,4#42'$2#%0#=,#H#E>!'%H-!23%!0-%2$;2:2"*,-A%
S(01*&0'$5#%("#/?/%5%)5IY$5%
d2*,>!%+*&%34#=7%V#/"6%H'%3%*(9:%!;*,-!;%$#%<#=*&$>%2%3)2#,/*4#$>%
+*("#I%;')*?.22%$#%*=9<%4-("7+3E'%)$2'E%*:E#494%!;*,*:-%
2%+,*:.')94%042>0#$-!;%0%/,4#42'$2#)26%$2'/"9,0-%0%$2!;%!07("*%$2'%
0=<#(0#E>%(27%&*%.'/#,0#%$#"-!;)2#("%+*%&*0$#$23%3,#03A%g0'/#$2'%
)*H'%E'&$#/%+*=*,(0-I%(-"3#!E7A%Q,0'&<3H#E>!'%(27%/,4#42'$2'%!0#(')%
+,*4#&02%&*%3(0/*&0'$2#%("#494%.3:%)278$2A%l,4#42'$2'6%/"9,'%$2'%
E'("%(0-:/*%.'!0*$'6%)*H'%"'H%4-)#=#I%/2./3&$2*4'=*6%#%$#4'"%
/2./3"-=*&$2*4'=*%+*&#4#$2#%!0-$$2/#6%0#)2#("%E'&$*,#0*4'=*%
+*&#$2#6%/"9,'%+,#4&*+*&*:$2'%:-<*:-%4-("#,!0#E>!'6%=&-:-%+#!E'$"%
$#"-!;)2#("%0=<*(2<%(27%&*%.'/#,0#A%B'("%427!%$2'04-/.'%2("*"$'6%
#:-%*(*:-%!;*,'%$#%<#=*&$>%2%3)2#,/*4#$>%+*("#I%;')*?.22%:-<-%
:#&#$'%+,0'0%.'/#,0#%E#/%$#E(0-:!2'E6%=&-%"-./*%4-(">+2%/,4#42'$2'A%
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42&*!0$'6%#.'%)*=>%0#=,#H#I%H-!23A%B'("%427!%(0!0'=9.$2'%4#H$'6%
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*:'E,0#<%.'/#,0A
Wszystko
o hemofilii
Poradnik
dla
rodziny
9–12
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
8$A565"*,:'!$2'%$#E427/(0-)%,-0-/2')%042>0#$-)%0%+,0-E)*4#$2')%
/*$!'$",#"3%!0-$$2/#%/,0'+$27!2#%E'("%+*E#42'$2'%(27%2$;2:2"*,#A
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(3:("#$!E'%!;')2!0$'6%/"9,'%/,>H>%4'%/,42A%Q,0'!24!2#<#%"'%3(34#E>%
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Wszystko
o hemofilii
9–13
Poradnik
dla
rodziny
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
!0-$$2/#%3%&#$'E%*(*:-%(+#&#%+*$2H'E%XnA%a#/#%*(*:7%0#.2!0#)-%4"'&-%
&*%=,3+-%!;*,-!;%$#%!27H/>%+*("#I%;')*?.22A%
@:-%3$2/$>I%,-0-/#%4-(">+2'$2#%2$;2:2"*,#6%.'/#,0%.'!0>!-%*(*:7%
!;*,>%$#%<#=*&$>%.3:%3)2#,/*4#$>%+*("#I%;')*?.22%:7&02'%("#,#<%(276%
4%)2#,7%)*H.24*8!26%4-/*,0-("-4#I%2$$'%)'"*&-%.'!0'$2#6%
$+A%&'()*+,'(-$7%14%+,0-+#&/3%<#=*&$'E%+*("#!2%;')*?.22%@5%!0-%.'/2%
#$"-?:,-$*.2"-!0$'6%0#)2#("%+*%+,*("3%+*&#4#I%/*$!'$",#"%!0-$$2/#A%
% + !"#$%"&'()#*+,-./#+01234(-/+#2#+0<+!+523(-<=#%2!(-%#,*0&05#3%]H%
>*/513#$5#%/%A')*B<55E%Q0IYZ%V%^%8$A565"*,-=
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4-<>!0$2'%!;<*+!94A%_%&02'4!0-$/2%)*H'%4-(">+2I%E'&'$%
$2'+,#42&<*4-%!;,*)*(*)%oA%q&-%"#/%(27%("#$2'6%
&02'4!0-$/#%E'("%$*(2!2'./>%;')*?.22A%B#/*%$*(2!2'./#6%)*H'%
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!0-$$2/#%CDDD%.3:%Do6%!*%!;,*$2%+,0'&%;')*?.2>A%
T*(2!2'./2%;')*?.22%)*=>%E'&$#/%)2'I%+*02*)%!0-$$2/#%
/,0'+$27!2#%+*$2H'E%YMn%$*,)-6%+,0'0%!*%(>%4%"'E%(#)'E%
=,3+2'6%4%/"9,'E%0$#E&3E>%(27%!;<*+!-%0%<#=*&$>%+*("#!2>%
!;*,*:-A%R*=>%3%$2!;%4-("7+*4#I%/,4#42'$2#%2%)*H'%:-I%
/*$2'!0$'%.'!0'$2'%4%/.2$2!'%(/#0%/,4*"*!0$-!;A%
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/,4#42'$2'%)*H'%:-I%:#,&0*%*:?"'A%P%+,0-+#&/3%0#:2'=3%
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% + !"#$%"&'()#*+,-./#+01234(-/+=#%2!(-%%,*0&05#3%TH% 6@#/*/'%
$*(5!5'<15%A')*B<55=
Wszystko
o hemofilii
Poradnik
dla
rodziny
9–14
9
!"#$%!&'&()'!*+#,!%!&
-#./!0&12)#34''
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& &9=8)&/*=2?!&-!)'@/!0&,&=,'7=+(&=&6!"#$%7&
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!;*,*:-`%$2'/"9,-)%0%$2!;%)*H'%$#4'"%$2=&-%$2'%:-I%+*&#4#$-%
!0-$$2/%/,0'+$27!2#A%D("$2'E>%E'&$#/%4-E>"/2A%_%$2'/"9,-!;%*(9:%
0%<#=*&$>%2%3)2#,/*4#$>%+*("#!2>%;')*?.22%)*=>%4-("7+*4#I%
/,4#42'$2#%"#/2'6%E#/%3%!;*,-!;%$#%!27H/>%+*("#IA%
l,4#42'$2#%3%*(9:%!;*,-!;%$#%<#=*&$>%2%3)2#,/*4#$>%+*("#I%
;')*?.22%)*=>%:-I%+*4#H$'6%$#4'"%E'8.2%4-("7+3E>%,0#&/*A%a#/%
$#+,#4&7%4%+'42'$%(+*(9:%<#=*&$#%2%3)2#,/*4#$#%+*("#I%
;')*?.22%:-4#%:#,&02'E%$2':'0+2'!0$#6%+*$2'4#H%!;*,-%2%E'=*%
,*&02$#%$2'%(+*&02'4#%(27%+,*:.')94%/,4*"*!0$-!;%2%4%042>0/3%
0%"-)%)*=>%*$'%:-I%$2'.'!0*$'A% +9]$2'$2#%4%.'!0'$23%+*=*,(0>%
(-"3#!E7%2%E'(0!0'%:#,&02'E%3",3&$2>%+*4,9"%&*%0&,*42#A%R*=>%"'H%
(+,#42I6%H'%4%E#/2)8%("*+$23%,*042$2'%(27%#,",*+#"2#A%
r*&02!'6%*+2'/3$*42'%2%(#)'%&02'!2%!;*,'%$#%;')*?.27%)3(0>%
$#3!0-I%(27%,*0+*0$#4#I%*0$#/2%/,4#42'F6%#:-%(0-:/*%
0#("*(*4#I%.'!0'$2'A%
G02'!2%!;*,'%$#%<#=*&$>%2%3)2#,/*4#$>%+*("#I%;')*?.22%
+*42$$-%0$#E&*4#I%(27%+*&%*+2'/>%*8,*&/#%.'!0'$2#%;')*?.226%
=&02'%,*&02$#%)*H'%30-(/#I%4(0'./2'%+*",0':$'%2$V*,)#!E'%*%"'E%
(/#02'%/,4*"*!0$'EA%
T2'/"9,0-%!;*,0-%$#%3)2#,/*4#$>%2%<#=*&$>%;')*?.27%4-)#=#E>%
("#<'=*%.3:%*/,'(*4'=*%.'!0'$2#%&*)*4'=*6%#%$2'/"9,0-%$#4'"%
,'=3.#,$'E%+,*?.#/"-/2A
Wszystko
o hemofilii
9–15
Poradnik
dla
rodziny